BookMasaki Nio, editor.
Summary: This book offers a comprehensive overview of the latest standard medical procedures and surgical techniques for biliary atresia (BA), as well as the perioperative care, long-term follow-up and transitions. Experts on pediatrics in such fields as hepatology, surgery, pathology, and liver transplantation present their research findings and analyses of this rare and intractable disease of unknown etiology. In Japan, shared experience and sound understanding based on conferences and guidelines have led to standardization of management and clinical care and, as a result, better outcomes. Providing insights into improving surgical outcomes, and including special chapters focusing on social support systems for patients and families as well as recent advances in early diagnosis, this book a valuable resource for medical professionals around the globe who are involved in treating biliary atresia. It is especially useful for pediatric hepatologists, pediatric surgeons and transplant surgeons.
Contents:
Biliary Atresia: A Historical Overview
History of The Japanese Biliary Atresia Society (JABS)
Japanese Biliary Atresia Registry (JBAR)
Pathogenesis: Overview
Pathogenesis: Genetics/Epigenetics
Pathogenesis: Viral Infection
Pathogenesis: Maternal Microchimerism
Epidemiology: Incidence and Gender Ratio
Epidemiology: Ethnic Variations/Family Histories/Heredity
Epidemiology: Gestational Age/Birth Weight /Associated Anomalies
Classifications
Mass Screening
Stool Color Card System
Prenatal Diagnosis and Signs/Symptoms
Intracranial Hemorrhage
Pathology
Biomarkers
Differential Diagnosis
Diagnostic Modalities
Preoperative Management and Direct Cholangiography
Operative Procedures: Open Kasai Procedure
Operative Procedures: Laparoscopic Kasai Procedure
Operative Procedures: Re-do Kasai Procedure
Operative Procedures: Cadaveric Liver Transplantation
Operative Procedures: Living Donor Liver Transplantation
Medical Treatment: UDCA/Steroid
Medical Treatment: Kampo Medicine
Prevention/Treatment of Postoperative Cholangitis
Nutritional Support
Protocols of Follow-up Management
Prognostic Indicators
Long-term Complications: Gastro-Esophageal Varices
Long-term Complications: Hypersplenism
Long-term Complications: Cholangitis/Gall Stones
Long-term Complications: Hepatopulmonary Syndrome
Long-term Complications: Portopulmonary Hypertension
Long-term Complications: Liver Cirrhosis/Hepatic Encephalopathy
Long-Term Results, General
Long-Term Results, Deformity of Intrahepatic Bile Ducts
Long-Term Results, Social Performance
Long-Term Results, Liver Transplantation
Biliary Atresia and Pregnancy/Delivery
Biliary Atresia and Malignancy
Future Prospects
Transition in Biliary Atresia
Society of Patients and Families
Clinical Guidelines for Biliary Atresia.